چکیده (انگلیسی):

Undifferentiated embryonal sarcoma of the liver (UESL) is a rare primary liver
tumor. Less than 100 adult cases were reported. It has female and right lobe preponderance.
In pathological features, focal osteoid picture in UESL is never reported. We present a 63-yearold
male patient with left lobe UESL with focal osteoid picture. He was admitted for a palpable
solid mass, with left upper quadrant abdominal pain for 4 months. Abdominal computed
tomography showed a huge well-circumscribed mass at left upper quadrant, 21.3
13
27.9 cm3
in size, with multiple septa in delayed phase. En bloc resection including lateral segmentectomy,
splenectomy, and cholecystectomy were performed, but tumor rupture was noted. The
pathologic diagnosis was ruptured UESL. The postoperative course was uneventful, and adjuvant
radiotherapy without chemotherapy was performed. Peritoneal seeding with massive
ascites was noted in the 9th month after operation. Even after receiving salvage chemotherapy,
he died 1 year after operation. Early complete surgical resection with adjuvant chemotherapy
may improve prognosis of UESL. But the overall survival of UESL did not improve until recently.
We present this case along with a literature review of the clinical pictures, diagnosis,
pathology presentation, pathologicogenesis of focal osteoid picture, treatment, and prognosis
for UESL of another 23 new reported cases since 2007.